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ABCB11

receptor: FXRTier 1

Drug substrates

drugs causing cholestasis (bosentan, cyclosporine, estrogens)

refs: 25198545

CAMIP causal chains

FXR

Disrupted receptor-mediated transactivation via the FXR/RXRα heterodimer, abolishing the critical canalicular expression of the Bile Salt Export Pump. This directly cripples the ATP-dependent rate-limiting step of hepatic bile acid elimination, precipitating toxic intracellular bile salt accumulation and rendering hepatocytes profoundly vulnerable to severe drug-induced cholestatic liver injury under medications such as bosentan and cyclosporine.

Affected substrate drugs (PharmGKB): bosentan; cyclosporine; estrogens

Scored variants near ABCB11

chr2:168,820,780..169,131,324, gene body plus 100 kb. Showing the strongest 200 by effect size.

VariantPosition PXR FXR AhR AF
chr2_169031334_A_Gchr2:16903133447,71218,97620,864—   
chr2_169031340_A_Gchr2:16903134045,24820,96020,736—   
chr2_169031342_T_Cchr2:16903134231,55212,41616,256—   
chr2_169031312_T_Achr2:16903131222,33614,35231,872—   
chr2_169031317_A_Gchr2:16903131721,1209,12010,496—   
chr2_169031312_T_Gchr2:16903131219,58411,53625,216—   
chr2_169031343_C_Gchr2:16903134318,8806,84812,096—   
chr2_169031315_T_Gchr2:16903131518,0169,47215,104—   
chr2_169031224_C_Gchr2:169031224-15,744-7,584-13,440—   
chr2_169031254_G_Tchr2:16903125415,6806,1126,272—   
chr2_169031341_T_Gchr2:16903134115,6807,6806,912—   
chr2_169031224_C_Achr2:169031224-15,552-7,312-14,400—   
chr2_169031326_A_Tchr2:169031326-14,400-6,880-11,520—   
chr2_169031282_A_Cchr2:16903128214,0807,0726,528—   
chr2_169031223_A_Cchr2:169031223-13,952-6,400-14,592—   
chr2_169031338_G_Tchr2:169031338-13,792-6,912-8,960—   
chr2_169031225_C_Achr2:169031225-13,568-6,336-9,920—   
chr2_169031223_A_Tchr2:169031223-13,504-5,952-13,056—   
chr2_169031308_T_Cchr2:16903130813,2486,2086,912—   
chr2_169031290_T_Cchr2:169031290-12,800-8,128-11,008—   
chr2_169031315_T_Cchr2:169031315-12,672-6,336-11,712—   
chr2_169031314_T_Cchr2:169031314-12,192-6,528-9,856—   
chr2_169031312_T_Cchr2:16903131211,8085,26411,008—   
chr2_169031288_T_Achr2:169031288-11,008-5,984-12,992—   
chr2_169031224_C_Tchr2:169031224-10,944-5,984-10,496—   
chr2_169031288_T_Cchr2:169031288-10,720-6,192-13,312—   
chr2_169031292_A_Gchr2:16903129210,6886,9449,344—   
chr2_169031313_T_Cchr2:169031313-10,432-5,376-11,008—   
chr2_169031336_C_Gchr2:169031336-10,432-4,368-10,304—   
chr2_169031338_G_Achr2:169031338-10,336-4,512-5,760—   
chr2_169031302_C_Gchr2:16903130210,0166,4649,088—   
chr2_169031262_G_Cchr2:1690312629,4723,4245,120—   
chr2_169031223_A_Gchr2:169031223-9,408-4,416-8,640—   
chr2_169031194_G_Cchr2:1690311949,3443,2323,392—   
chr2_169031308_T_Gchr2:1690313089,3445,6328,832—   
chr2_169031340_A_Tchr2:1690313409,3443,5526,272—   
chr2_169031254_G_Cchr2:1690312549,2163,4883,840—   
chr2_169031334_A_Tchr2:169031334-9,024-4,064-6,272—   
chr2_169031333_G_Tchr2:169031333-8,864-4,128-6,400—   
chr2_169031325_A_Tchr2:169031325-8,800-3,776-7,040—   
chr2_169031317_A_Tchr2:169031317-8,768-3,968-7,168—   
chr2_169031291_C_Tchr2:169031291-8,672-5,408-10,240—   
chr2_169031336_C_Achr2:169031336-8,576-2,864-9,728—   
chr2_169031306_C_Tchr2:169031306-8,448-4,480-6,848—   
chr2_169031289_T_Achr2:169031289-8,384-5,824-10,048—   
chr2_169031309_C_Tchr2:169031309-8,224-4,048-6,016—   
chr2_169031226_T_Cchr2:169031226-8,192-3,424-4,608—   
chr2_169031226_T_Achr2:169031226-8,128-3,744-3,968—   
chr2_169031329_C_Achr2:169031329-8,128-3,328-4,928—   
chr2_169031294_A_Tchr2:169031294-8,096-6,144-10,624—   
chr2_169031225_C_Tchr2:169031225-8,064-3,840-3,968—   
chr2_169031341_T_Achr2:1690313418,0641,8245,120—   
chr2_169031324_T_Cchr2:1690313247,7763,7442,944—   
chr2_169031331_C_Achr2:169031331-7,648-3,328-8,320—   
chr2_169031295_A_Tchr2:169031295-7,552-4,064-11,072—   
chr2_169031198_T_Gchr2:169031198-7,488-2,752-3,328—   
chr2_169031290_T_Gchr2:1690312907,4243,1044,352—   
chr2_169031336_C_Tchr2:169031336-7,360-2,992-6,592—   
chr2_169031343_C_Achr2:169031343-7,168-2,416-5,440—   
chr2_169031322_T_Achr2:1690313227,0722,8164,096—   
chr2_169031184_A_Cchr2:1690311847,0402,2085,760—   
chr2_169031270_C_Tchr2:169031270-7,040-3,008-2,816—   
chr2_169031342_T_Achr2:1690313426,9762,6564,480—   
chr2_169031304_A_Cchr2:169031304-6,912-3,152-5,504—   
chr2_169031292_A_Tchr2:169031292-6,848-4,192-7,040—   
chr2_169031291_C_Gchr2:169031291-6,816-4,800-8,832—   
chr2_169031320_A_Cchr2:169031320-6,528-3,776-6,848—   
chr2_169031321_T_Achr2:169031321-6,464-4,160-6,592—   
chr2_169031260_A_Tchr2:1690312606,4641,7283,072—   
chr2_169031293_C_Gchr2:169031293-6,400-5,440-8,960—   
chr2_169031309_C_Achr2:169031309-6,240-3,776-4,224—   
chr2_169031225_C_Gchr2:169031225-6,080-2,816-832—   
chr2_169031339_A_Gchr2:1690313396,0482,4004,224—   
chr2_169031291_C_Achr2:169031291-5,888-4,416-7,424—   
chr2_169031290_T_Achr2:1690312905,8882,1123,968—   
chr2_169031176_T_Achr2:1690311765,8241,6642,240—   
chr2_169031267_C_Gchr2:1690312675,8242,7525,632—   
chr2_169031296_C_Achr2:169031296-5,760-3,888-9,280—   
chr2_169031178_A_Cchr2:1690311785,7602,1122,624—   
chr2_169031226_T_Gchr2:169031226-5,760-2,112-3,072—   
chr2_169031327_A_Gchr2:169031327-5,760-1,904-4,800—   
chr2_169031329_C_Gchr2:169031329-5,760-2,336-3,904—   
chr2_169031310_G_Achr2:169031310-5,728-2,912-3,840—   
chr2_169031313_T_Achr2:169031313-5,632-2,880-6,336—   
chr2_169031323_C_Achr2:169031323-5,600-3,136-6,080—   
chr2_169031278_A_Gchr2:1690312785,5682,2084,608—   
chr2_169031324_T_Gchr2:1690313245,4403,1684,992—   
chr2_169031279_G_Cchr2:169031279-5,376-1,952-4,032—   
chr2_169031292_A_Cchr2:169031292-5,376-3,904-5,248—   
chr2_169031288_T_Gchr2:169031288-5,344-3,440-8,640—   
chr2_169031294_A_Gchr2:169031294-5,280-4,544-8,960—   
chr2_169031327_A_Tchr2:169031327-5,280-1,888-5,888—   
chr2_169031293_C_Achr2:169031293-5,248-3,680-5,888—   
chr2_169031197_T_Cchr2:169031197-5,248-7681,984—   
chr2_169031305_A_Tchr2:169031305-5,248-2,592-4,992—   
chr2_169031264_A_Cchr2:169031264-5,216-1,920-512—   
chr2_169031289_T_Gchr2:169031289-5,120-4,000-6,208—   
chr2_169031316_C_Achr2:1690313165,1203521,664—   
chr2_169031311_G_Achr2:169031311-5,056-1,760-3,584—   
chr2_169031306_C_Achr2:169031306-5,024-2,976-3,584—   
chr2_169031335_A_Cchr2:1690313354,8962,6244,224—   
chr2_169031332_T_Gchr2:169031332-4,864-2,976-5,120—   
chr2_169031171_A_Cchr2:1690311714,8641,2802,496—   
chr2_169031315_T_Achr2:1690313154,8642,1442,560—   
chr2_169031337_A_Cchr2:1690313374,8642,0801,408—   
chr2_169031294_A_Cchr2:169031294-4,800-4,384-6,784—   
chr2_169031332_T_Achr2:169031332-4,800-3,424-5,760—   
chr2_169031179_A_Cchr2:1690311794,8008001,728—   
chr2_169031335_A_Tchr2:169031335-4,800-2,400-4,352—   
chr2_169031295_A_Cchr2:169031295-4,736-3,200-5,760—   
chr2_169031308_T_Achr2:1690313084,7362,0165,248—   
chr2_169031318_T_Cchr2:169031318-4,736-2,752-2,688—   
chr2_169031311_G_Cchr2:169031311-4,704-2,192-3,840—   
chr2_169031339_A_Cchr2:1690313394,6082,2721,152—   
chr2_169031326_A_Gchr2:1690313264,5761,9522,304—   
chr2_169031222_T_Gchr2:169031222-4,544-3,264-4,992—   
chr2_169031326_A_Cchr2:1690313264,5121,9843,328—   
chr2_169031260_A_Cchr2:1690312604,4801,1842,688—   
chr2_169031227_G_Cchr2:169031227-4,416-1,632-2,560—   
chr2_169031266_T_Cchr2:169031266-4,416-2,240-2,176—   
chr2_169008089_G_Tchr2:169008089-4,3845122,496—   
chr2_169031317_A_Cchr2:169031317-4,320-2,816-3,456—   
chr2_169031188_G_Tchr2:169031188-4,288-1,568-4,736—   
chr2_169031172_A_Cchr2:1690311724,2881,1842,432—   
chr2_169031241_G_Tchr2:1690312414,2881,4083,264—   
chr2_169031276_A_Tchr2:169031276-4,288-2,336896—   
chr2_169031296_C_Gchr2:169031296-4,224-2,432-6,400—   
chr2_169031258_T_Cchr2:169031258-4,224-1,152128—   
chr2_169031302_C_Tchr2:169031302-4,192-1,536-3,072—   
chr2_169031289_T_Cchr2:169031289-4,128-3,584-6,976—   
chr2_169031304_A_Tchr2:169031304-4,128-2,128-3,072—   
chr2_169031323_C_Tchr2:169031323-4,128-1,856-3,008—   
chr2_169031194_G_Tchr2:1690311944,0961,376896—   
chr2_169031337_A_Tchr2:1690313374,0001,6001,792—   
chr2_169031330_A_Gchr2:1690313303,9681,7921,664—   
chr2_169031299_T_Cchr2:169031299-3,904-2,048-3,968—   
chr2_169031247_G_Tchr2:1690312473,9041,5041,088—   
chr2_169031301_T_Cchr2:1690313013,9042,2083,200—   
chr2_169031307_C_Tchr2:169031307-3,872-2,208-4,672—   
chr2_169031245_A_Cchr2:1690312453,8401,5041,984—   
chr2_169031267_C_Achr2:1690312673,8401,0562,688—   
chr2_169008119_T_Achr2:1690081193,808800-128—   
chr2_169031311_G_Tchr2:169031311-3,808-1,392-3,136—   
chr2_169031216_G_Tchr2:1690312163,7761,4402,368—   
chr2_169031298_T_Cchr2:169031298-3,744-1,760-1,280—   
chr2_169031307_C_Achr2:169031307-3,712-1,952-3,904—   
chr2_169031194_G_Achr2:1690311943,7121,280-64—   
chr2_169031231_A_Cchr2:169031231-3,712-1,088-896—   
chr2_169031259_A_Gchr2:169031259-3,712-1,792-1,728—   
chr2_169031330_A_Cchr2:1690313303,6802,6563,712—   
chr2_169031186_G_Cchr2:1690311863,6488961,408—   
chr2_169031298_T_Achr2:169031298-3,648-2,048-2,432—   
chr2_169031325_A_Gchr2:1690313253,6161,8562,432—   
chr2_169031227_G_Tchr2:169031227-3,584-896-2,176—   
chr2_169031235_G_Tchr2:1690312353,5841,3122,048—   
chr2_169031241_G_Cchr2:1690312413,5841,9203,008—   
chr2_169031252_A_Cchr2:169031252-3,584-1,824-1,792—   
chr2_169031278_A_Cchr2:169031278-3,584-1,504-384—   
chr2_169031263_G_Cchr2:1690312633,5201,7924,224—   
chr2_169031173_G_Achr2:1690311733,5201,632128—   
chr2_169031227_G_Achr2:169031227-3,520-1,184-1,728—   
chr2_169031244_G_Achr2:1690312443,5201,1201,792—   
chr2_169031244_G_Cchr2:1690312443,5201,3442,560—   
chr2_169031176_T_Gchr2:1690311763,4561,0562,048—   
chr2_169031180_A_Tchr2:169031180-3,456-1,440-1,792—   
chr2_169031287_G_Achr2:1690312873,4562,4643,456—   
chr2_169008140_T_Gchr2:169008140-3,39264-96—   
chr2_169031239_T_Cchr2:1690312393,3921,5681,344—   
chr2_169031299_T_Gchr2:1690312993,3922881,536—   
chr2_169031313_T_Gchr2:169031313-3,328-2,240-4,736—   
chr2_169031263_G_Tchr2:1690312633,3281,9843,584—   
chr2_169008089_G_Achr2:169008089-3,3282241,024—   
chr2_169031318_T_Gchr2:169031318-3,296-1,728-2,688—   
chr2_169031232_T_Gchr2:169031232-3,264-1,344-4,032—   
chr2_169031284_A_Gchr2:169031284-3,264-1,280-3,712—   
chr2_169031174_A_Cchr2:1690311743,2646722,048—   
chr2_169031283_A_Tchr2:169031283-3,264-1,536-2,944—   
chr2_169008120_C_Tchr2:1690081203,232192-1,696—   
chr2_169008090_A_Tchr2:169008090-3,2001281,792—   
chr2_169031177_T_Gchr2:1690311773,2008642,112—   
chr2_169031200_G_Tchr2:1690312003,200832-704—   
chr2_169031220_C_Achr2:169031220-3,200-2,080-384—   
chr2_169031304_A_Gchr2:1690313043,2002,4322,368—   
chr2_169031167_A_Cchr2:1690311673,1365442,176—   
chr2_169031173_G_Cchr2:1690311733,136768896—   
chr2_169031278_A_Tchr2:169031278-3,136-1,024-1,152—   
chr2_169031303_C_Tchr2:1690313033,1041,5361,920—   
chr2_169031333_G_Cchr2:169031333-2,976-1,568-3,840—   
chr2_169031316_C_Tchr2:169031316-2,912-3,232-4,992—   
chr2_169031251_G_Tchr2:169031251-2,752-1,440-3,264—   
chr2_169031307_C_Gchr2:169031307-2,656-1,056-4,096—   
chr2_169008129_G_Cchr2:1690081292,240-576-4,256—   
chr2_169031314_T_Achr2:169031314-2,144-3,520-6,336—   
chr2_169031320_A_Gchr2:169031320-1,824-1,536-3,136—   
chr2_169031293_C_Tchr2:169031293-1,664-1,376-3,456—   
chr2_169031220_C_Tchr2:1690312201,4721283,200—   
chr2_169031287_G_Tchr2:169031287-1,344-1,376-4,352—   
chr2_169031295_A_Gchr2:169031295-1,312-2,048-4,608—   
chr2_169031280_T_Achr2:169031280-1,280-1,504-3,712—   
chr2_169031236_A_Cchr2:1690312364485763,200—   

Showing 200 of 200 in this window. Scores are the raw center bin Δ, ALT minus REF; click a column to sort.